Case study 10: Long term benefits for Fontan procedure

A Fontan procedure is an operation done for children who have heart abnormalities. The life expectancy of patients who undergo the Fontan procedure is unknown. The study evaluated the long term outcomes of patients who had Fontan surgery in Australia and New Zealand. The study reported excellent long term survival outcomes for patients.

How did the PHRN infrastructure help?
The Australian Institute of Health and Welfare linked the clinical data from the Australian and New Zealand Fontan Registry with the National Death Index for the research team to analyse.

Authors/Contributors
d'Udekem Y, Iyengar AJ, Galati JC, Forsdick V, Weintraub RG, Wheaton GR, Bullock A, Justo RN, Grigg LE, Sholler GF, Hope S, Radford DJ, Gentles TL, Celermajer DS, Winlaw DS.

Reference
d'Udekem Y, Iyengar AJ, Galati JC, Forsdick V, Weintraub RG, Wheaton GR, et al. Redefining expectations of long-term survival after the Fontan procedure: twenty-five years of follow-up from the entire population of Australia and New Zealand. Circulation. 2014;130(11 Suppl 1):S32-8. Access 12 April 2016 <http://circ.ahajournals.org/content/130/11_suppl_1/S32.abstract>